Human GLα Antibody Pair Set
Price:
Size:
50 μL & 100 μg
- 反应性： Human
| Background |
GLA,also named as Melibiase,Agalsidase and Alpha-galactosidase A,belongs to the glycosyl hydrolase 27 family. It hydrolyzes terminal,non-reducing alpha-D-galactose residues in alpha-D-galactosides,including galactose oligosaccharides,galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resulting from the deficient activity of GLA. Enzyme replacement therapy (ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease,a lysosomal storage disease.
|
| Synonyms |
GLA;Agalsidase;Alpha-galactosidase A;Alpha-D-galactosidase A;Alpha-D-galactoside galactohydrolase;Galactosylgalactosylglucosylceramidase GLA
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| Swissprot | |
| Reactivity |
Human
|
| Specificity |
Detects Human GLα in ELISAs
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| Buffer |
Capture Antibody:PBS with 0.04% Proclin 300, 50% glycerol, pH 7.4; Detection Antibody:PBS with 0.04% Proclin 300, 1% protective protein, 50% glycerol, pH 7.4
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| Storage |
-20℃
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| Expiration date |
12个月
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