GLα/Galactosidase Alpha Polyclonal Antibody
Price:
Size:
100 μL
25 μL
- 宿主： Rabbit
- 反应性： Human
- 应用性： WB;IHC
| Verified Samples |
Verified Samples in WB: MCF-7, 293T Verified Samples in IHC: Human liver |
| Dilution | WB 1:500-1:1000, IHC 1:1000-1:2000 |
| Clonality | Polyclonal |
| Isotype | IgG |
| Immunogen | Recombinant Human GLα/Galactosidase Alpha protein expressed by Mammalian |
| Abbre | GLα |
| Synonyms | GLA, GALA, Alpha-D-Galactoside, Galactohydrolase, galactosidase alpha, GLAL, Melibiase, Agalsidase, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, Galactosylgalactosylglucosylceramidase GLA |
| Swissprot | |
| Calculated MW | 49 kDa |
| Observed MW | 49 kDa |
| Cellular Localization | Lysosome |
| Concentration | 1 mg/mL |
| Storage | Store at -20°C Valid for 12 months. Avoid freeze / thaw cycles. |
| Buffer | PBS with 0.05% proclin 300, 1% protective protein and 50% glycerol,pH7.4 |
| Purification Method | Antigen Affinity Purification |
| Research Areas | Cardiovascular |
| Conjugation | Unconjugated |
| Background | alpha -Galactosidase A is a homodimeric glycoprotein that can release terminal alpha -galactosyl moieties from glycolipids and glycoproteins and catalyze the hydrolysis of melibiose into galactose and glucose . It is a lysosomal enzyme and is responsible for degradation of glycolipid globotriaosylceramide (Gb3) (Gal alpha 1‑4Gal beta 1‑4Glc beta ‑ceramide). Mutations in this gene cause Fabry disease, an X-linked hereditary lysosomal storage disease with the accumulation of Gb3 in the walls of small blood vessels, nerves, dorsal root ganglia, renal glomerular and tubular epithelial cells, and cardiomyocytes. |
Western blot with Anti GLα/Galactosidase Alpha Polyclonal antibody at dilution of 1:1000. Lane 1: MCF-7 cell lysate, Lane 2: 293T cell lysate.
Immunohistochemistry of paraffin-embedded Human liver using GLα/Galactosidase Alpha Polyclonal Antibody at dilution of 1:1500.
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